[Pachydermoperiostosis (Touraine-Solente-Golé syndrome). Case report].
نویسندگان
چکیده
Pachydermoperiostosis or primary hypertrophic osteoarthropathy, also known as Touraine-Solente-Golé syndrome, is a rare process, frequently inherited. In its complete form it is characterized by pachydermia (thickening of the skin), skeletal changes (periostosis) and acropachia (digital clubbing). We report a patient that consulted for skeletal symptoms, as the acropachia and cutaneous manifestations (thickening of the skin of the face, scalp, hands and feet) went unnoticed due to their slow and progressive development. We review the characteristic features of this syndrome. We highlight the importance of ruling out secondary forms of hypertrophic osteoarthropathy and of a close follow-up of these patients because of complications that might develop on the long-term.
منابع مشابه
[Pachydermoperiostosis (Touraine-Solente-Gole syndrome)].
We report on a 38-year-old male patient suffering from pachydermoperiostosis (Touraine-Solente-Golé Syndrome), who underwent a cosmetic operation without success.
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Hypertrophic Osteoarthropathy secondary to various causes is not a common entity but primary hypertrophic osteoarthropathy (also called Touraine-Solente-Gole Syndrome) is an extremely rare genetic disorder. It was first described in 1868 by Friedrich and has premier features of clubbing, periostosis and pachydermia. Based on clinical manifestations Touraine Solente and Gole distinguished it int...
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ورودعنوان ژورنال:
- Actas dermo-sifiliograficas
دوره 98 2 شماره
صفحات -
تاریخ انتشار 2007